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Tuber cinereum hamartoma is a benign tumor … Tuber cinereum hamartoma is a benign tumor in which a disorganized collection of neurons and glia accumulate at the tuber cinereum of the hypothalamus on the floor of the third ventricle. It is a congenital malformation, included on the spectrum of gray matter heterotopias. Formation occurs during embryogenesis, typically between days 33 and 41 of gestation. Size of the tumor varies from one to three centimeters in diameter, with the mean being closer to the low end of this range. It is estimated to occur at a frequency of one in one million individuals.equency of one in one million individuals.
, Hamartoma podwzgórza (ang. hypothalamic ha … Hamartoma podwzgórza (ang. hypothalamic hamartoma, HH) – wrodzony, nienowotworowy guz podwzgórza, objawiający się klinicznie triadą objawów: napadami śmiechu (ang. gelastic seisures), przedwczesnym dojrzewaniem płciowym i opóźnieniem rozwoju. Niekiedy, w związku z uciskiem guza na skrzyżowanie wzrokowe, pojawiają się zaburzenia widzenia.rokowe, pojawiają się zaburzenia widzenia.
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rdfs:comment |
Tuber cinereum hamartoma is a benign tumor … Tuber cinereum hamartoma is a benign tumor in which a disorganized collection of neurons and glia accumulate at the tuber cinereum of the hypothalamus on the floor of the third ventricle. It is a congenital malformation, included on the spectrum of gray matter heterotopias. Formation occurs during embryogenesis, typically between days 33 and 41 of gestation. Size of the tumor varies from one to three centimeters in diameter, with the mean being closer to the low end of this range. It is estimated to occur at a frequency of one in one million individuals.equency of one in one million individuals.
, Hamartoma podwzgórza (ang. hypothalamic ha … Hamartoma podwzgórza (ang. hypothalamic hamartoma, HH) – wrodzony, nienowotworowy guz podwzgórza, objawiający się klinicznie triadą objawów: napadami śmiechu (ang. gelastic seisures), przedwczesnym dojrzewaniem płciowym i opóźnieniem rozwoju. Niekiedy, w związku z uciskiem guza na skrzyżowanie wzrokowe, pojawiają się zaburzenia widzenia.rokowe, pojawiają się zaburzenia widzenia.
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rdfs:label |
Tuber cinereum hamartoma
, Hamartoma podwzgórza
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