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http://dbpedia.org/resource/Pseudocholinesterase_deficiency
http://dbpedia.org/ontology/abstract Pseudocholinesterase deficiency is an autoPseudocholinesterase deficiency is an autosomal recessive inherited blood plasma enzyme abnormality in which the body's production of butyrylcholinesterase (BCHE; pseudocholinesterase aka PCE) is impaired. People who have this abnormality may be sensitive to certain anesthetic drugs, including the muscle relaxants succinylcholine and mivacurium as well as other ester local anesthetics. as well as other ester local anesthetics. , عجز الكولين استراز الكاذب أو نقص الكولين اعجز الكولين استراز الكاذب أو نقص الكولين استراز الكاذب (بالإنجليزية: Pseudocholinesterase deficiency)‏ هو شذوذ وراثي يتميز بنقص إنتاج إنزيم الكولين استراز الكاذب في بلازما الدم. ويمكن أن يكون لدى الأشخاص المصابين بنقص هذا الإنزيم حساسية لبعض الأدوية المخدرة، بما في ذلك مرخيات العضلات مثل السكسنيل كولين وكلوريد ميفاكوريام وغير ذلك من مخدرات الإسترات الموضعية.ريام وغير ذلك من مخدرات الإسترات الموضعية.
http://dbpedia.org/ontology/complications Apnea, Sudden cardiac death
http://dbpedia.org/ontology/diseasesDB 10829
http://dbpedia.org/ontology/eMedicineSubject med
http://dbpedia.org/ontology/eMedicineTopic 1935
http://dbpedia.org/ontology/icd9 289.89
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http://dbpedia.org/property/causes Autosomal Recessive
http://dbpedia.org/property/complications Apnea, Sudden cardiac death
http://dbpedia.org/property/diagnosis Prolonged recovery from paralysis in self or blood relative
http://dbpedia.org/property/diseasesdb 10829
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http://dbpedia.org/property/name Pseudocholinesterase deficiency
http://dbpedia.org/property/omim 177400
http://dbpedia.org/property/onset Cocaine use, Administration of plasma cholinesterase metabolized pharmaceuticals
http://dbpedia.org/property/prevention Alternative neuromuscular blockade agents, cocaine avoidance
http://dbpedia.org/property/symptoms Prolonged paralysis
http://dbpedia.org/property/treatment Mechanical ventilation
http://dbpedia.org/property/types Homozygous; Heterezygous: Silent, Absent, Fluoride, Dibucaine
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rdfs:comment Pseudocholinesterase deficiency is an autoPseudocholinesterase deficiency is an autosomal recessive inherited blood plasma enzyme abnormality in which the body's production of butyrylcholinesterase (BCHE; pseudocholinesterase aka PCE) is impaired. People who have this abnormality may be sensitive to certain anesthetic drugs, including the muscle relaxants succinylcholine and mivacurium as well as other ester local anesthetics. as well as other ester local anesthetics. , عجز الكولين استراز الكاذب أو نقص الكولين اعجز الكولين استراز الكاذب أو نقص الكولين استراز الكاذب (بالإنجليزية: Pseudocholinesterase deficiency)‏ هو شذوذ وراثي يتميز بنقص إنتاج إنزيم الكولين استراز الكاذب في بلازما الدم. ويمكن أن يكون لدى الأشخاص المصابين بنقص هذا الإنزيم حساسية لبعض الأدوية المخدرة، بما في ذلك مرخيات العضلات مثل السكسنيل كولين وكلوريد ميفاكوريام وغير ذلك من مخدرات الإسترات الموضعية.ريام وغير ذلك من مخدرات الإسترات الموضعية.
rdfs:label عجز الكولين استراز الكاذب , Pseudocholinesterase deficiency
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