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Http://dbpedia.org/resource/Fibro-adipose vascular anomaly
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http://dbpedia.org/resource/Fibro-adipose_vascular_anomaly
http://dbpedia.org/ontology/abstract Fibro-adipose vascular anomaly, also knownFibro-adipose vascular anomaly, also known as FAVA, is a type of vascular anomaly that is both rare and painful. FAVA is characterized by tough fibrofatty tissue taking over portions of muscle, most often contained within a single limb. FAVA also causes venous and/or lymphatic abnormalities. Though FAVA has only been recognized as a distinct vascular anomaly, separate from common venous malformations, within the past ten years, FAVA a distinct congenital disorder.ears, FAVA a distinct congenital disorder. , Anomalia Vascular Fibro-Adiposa (AVFA), é uma doença congênita caracterizada por alterações musculares fibro-adiposas e canais venosos dilatados (flebectasia), causando dor e contratura local.
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http://dbpedia.org/ontology/medication http://dbpedia.org/resource/Sirolimus +
http://dbpedia.org/ontology/symptom http://dbpedia.org/resource/Contracture + , http://dbpedia.org/resource/Pain +
http://dbpedia.org/ontology/synonym FAVA
http://dbpedia.org/ontology/treatment http://dbpedia.org/resource/Surgical_resection + , http://dbpedia.org/resource/Cryoablation + , http://dbpedia.org/resource/Physical_therapy +
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http://dbpedia.org/property/causes Unknown, potentially genetic
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http://dbpedia.org/property/onset Later childhood to young adulthood
http://dbpedia.org/property/specialty http://dbpedia.org/resource/Pediatrics + , http://dbpedia.org/resource/Interventional_radiology +
http://dbpedia.org/property/symptoms Pain, difficulty moving the affected limb, contracture, mild enlargement of the affected limb
http://dbpedia.org/property/synonym FAVA
http://dbpedia.org/property/treatment Physical therapy, surgical resection, cryoablation
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rdfs:comment Fibro-adipose vascular anomaly, also knownFibro-adipose vascular anomaly, also known as FAVA, is a type of vascular anomaly that is both rare and painful. FAVA is characterized by tough fibrofatty tissue taking over portions of muscle, most often contained within a single limb. FAVA also causes venous and/or lymphatic abnormalities. Though FAVA has only been recognized as a distinct vascular anomaly, separate from common venous malformations, within the past ten years, FAVA a distinct congenital disorder.ears, FAVA a distinct congenital disorder. , Anomalia Vascular Fibro-Adiposa (AVFA), é uma doença congênita caracterizada por alterações musculares fibro-adiposas e canais venosos dilatados (flebectasia), causando dor e contratura local.
rdfs:label Anomalia vascular fibroadiposa , Fibro-adipose vascular anomaly
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